Section: 
Otiology
OtiologyClinical observation of intraoperative detection of intracochlear schwannoma during cochlear implantation
V. E. Kuzovkov (1), A. S. Lilenko (2), S. B. Sugarova (3), V. A. Tanaschishina (4), P. R. Kharitonova (5)
(1), (2), (3), (4), (5) Saint Petersburg Research Institute of Ear, Throat, Nose and Speech, Saint Petersburg, 190013, Russian Federation
UDK: УДК 616.283.1-089.843:616.282.1-006.385
DOI: https://doi.org/10.18692/1810-4800-2024-5-64-72
ABSTRACT
Resume. Intralabyrinthine schwannomas are rare tumors. Only 500 cases of intralabyrinthine schwannomas have been described in the literature, including 100 cases of intracochlear neurinomas. Patients and methods. A 42-year-old patient with progressive hearing loss over the past 10 years was admitted to the Saint Petersburg ENT Research Institute. At the time of treatment, the subject had profound bilateral chronic sensorineural hearing loss with insignificant residual hearing in the right ear. The hearing aid was ineffective for a year and a half. The patient repeatedly underwent cranial trepanation for meningiomas in the frontotemporal and posterior surface of the pyramid of the right temporal bone, also the patient’s anamnesis includes Lues from 1998. Computed tomography of the temporal bones showed no signs of inflammatory and destructive changes in the structures of the middle ear. The cochlear ducts were patent bilaterally. When performing cochlear implantation on the right ear, the insertion of an electrode was impossible due to obliteration of the lumen of the spiral canal of the cochlea. A mucofibrous growth was visualized in the lumen of the U-turn of the cochlea. The descending part of the basal turn was drilled-out with the diamond burrs for about 2 mm. The fibrous-mucous formation has been removed. The active electrode was completely inserted into the cochlea. Conclusion. Despite the intraoperative difficulties at the time of the insertion of the electrode array, cochlear implantation in patients with neurofibromatosis type II enables good results of aural rehabilitation.
Publication date:
17.10.2024
Keywords:
cochlear implantation, neurofibromatosis type II, intralabyrinthine schwannoma, the cochlea basal turn For citation:
Kuzovkov V. E., Lilenko A. S., Sugarova S. B., Tanaschishina V. A., Kharitonova P. R. Clinical observation of intraoperative detection of intracochlear schwannoma during cochlear implantation. Russian Otorhinolaryngology. 2024;23(5):64-72. (In Russ.) https://doi.org/10.18692/1810-4800-2024-5-64-72